craniosynostosis


craniosynostosis
or craniostosis

Cranial deformity produced when the bones of the skull fuse too early.

Pressure from the growing brain normally causes the skull bones to grow along the seams (cranial sutures) between them. If all the sutures fuse early, the head remains abnormally small, which can cause mental retardation or blindness. If only one or some fuse early, the skull grows in other directions and becomes deformed. Surgery in the first two years to keep the sutures open longer minimizes these complications.

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also called  craniostosis 

      any of several types of cranial deformity—sometimes accompanied by other abnormalities—that result from the premature union of the skull vault bones. Craniosynostosis is twice as frequent in males than in females and is most often sporadic, although the defect may be familial.

      Normally, the skull bones grow in response to pressure from the growing brain; growth occurs along the cranial sutures perpendicularly to the long axis of the suture. If the brain fails to grow or if all the sutures fuse early, an abnormally small head results. Of the various sutures, the sagittal (front to back along the top midline of the skull) most frequently fuses prematurely. Because the skull then cannot grow in width, the vault becomes long, high, and narrow (scaphocephaly). If the coronal suture (side to side near the front) fuses early, the skull becomes short front to back but wide and high (oxycephaly). Apert syndrome ( acrocephalosyndactyly) is a rare inherited disorder in which premature closure of the coronal suture is associated with fused digits, defects of the brain and face, and sometimes other abnormalities. With premature closure of both sagittal and coronal sutures, growth occurs only vertically, and a tower-shaped skull develops. Crouzon syndrome is a rare inherited disorder characterized by the fusing of the coronal, sagittal, and sometimes lamboid (side to side posteriorly) sutures, undergrowth of the upper jaw, and other deformities. Premature closure of the metopic suture (which separates the frontal bone into halves for the first two years of life) produces a triangularly shaped head (trigonocephaly) and may be accompanied by brain damage.

      Surgical procedures within the first two years of life minimize the deformities and decrease the possibility of such complications as mental retardation and blindness by allowing the sutures to remain in the open position until brain growth is complete.

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Universalium. 2010.

Look at other dictionaries:

  • Craniosynostosis — Classification and external resources Child with premature closure (craniosynostosis) of the lambdoid suture. Notice the swelling on the right side of the head ICD 10 …   Wikipedia

  • Craniosynostosis — Premature fusion of the cranial sutures (the fibrous joints between the bones of the skull) in an infant, preventing normal growth of the baby s head. Craniosynostosis involving some but not all of the sutures causes an abnormally shaped skull.… …   Medical dictionary

  • craniosynostosis — n. premature fusion of some of the cranial bones, usually before birth, so that the skull is unable to expand in certain directions to assume its normal shape under the influence of the growing brain. Depending on which cranial sutures fuse early …   The new mediacal dictionary

  • Craniosynostosis — priešlaikinis kaukolės siūlių sukalkėjimas statusas T sritis embriologija atitikmenys: lot. Craniosynostosis ryšiai: platesnis terminas – mažagalvystė sinonimas – kaukolės sinostozė …   Medicininės histologijos ir embriologijos vardynas

  • craniosynostosis — noun Etymology: New Latin Date: 1951 premature fusion of the sutures of the skull …   New Collegiate Dictionary

  • craniosynostosis — noun a medical condition in which some or all of the sutures in the skull of an infant close too early, causing problems with normal brain and skull growth. Syn: cloverleaf skull, cloverleaf skull syndrome, kleeblattschadel …   Wiktionary

  • craniosynostosis — /kreɪnioʊsaɪnoʊˈstoʊsəs/ (say krayneeohsuynoh stohsuhs) noun a congenital condition in which one or more sutures of the skull prematurely fuse, causing an irregular skull shape …   Australian English dictionary

  • Craniosynostosis–anal anomalies–porokeratosis syndrome — Classification and external resources OMIM 603116 Craniosynostosis–anal anomalies–porokeratosis syndrome (also known as CAP syndrome ) is a cutaneous condition inherited in an autosomal recessive fashion.[1] …   Wikipedia

  • Краниосиностоз (Craniosynostosis) — преждевременное сращение некоторых костей черепа, происходящее обычно еще до рождения ребенка, в результате которого череп не может расшириться в отдельных направлениях и принять нормальную форму, необходимую для растущего мозга. В зависимости от …   Медицинские термины

  • clinocephaly — Craniosynostosis in which the upper surface of the skull is concave, presenting a saddle shaped appearance in profile. SYN: saddle head. [clino + G. kephale, head] * * * cli·no·ceph·a·ly (kli″no sefґə le) [clino + cephaly] congenital… …   Medical dictionary


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